贝赫切特综合征的肺表现

PULMONARY MANIFESTATION OF BEHCET'S DISEASE

133例贝赫切特综合征（Behcetsyndrome，BS）中20例有肺部病变（6．7％），多见于中、青年。男性稍多，一般于BS肺外病变后3．8年起病。主要临床表现为咳嗽、咯血、气短、胸痛、反复发热。3例以肺部病变为首发临床表现。X线胸片异常18例，用肾上腺皮质激素及免疫抑制剂治疗有效。V／Q显象、免疫病理、胸部增强CT、MRI、血管造影及肺功能测定将有助诊断。

20 out of 133 cases with Bechcet syndrome had pulmonary involvement. Resurrent episodes of couph,hemoptysis, dyspnea, chest pain and fever were the primary clinical signs. 3 cases had pulmonary involvement as the first manifestation of the disease. Chest X-ray films showed pulmonary infiltrates in 18 cases. The perfusion ventilation scan, angiogra phy, enhanced CT scan and MRI of the chest, immunopathologic and pulmonary function test would be helpful to the confirmation of the diagnosis.