超声诊断隆突性皮肤纤维肉瘤

Ultrasonographic diagnosis of dermatofibrosarcoma protuberans

目的探讨隆突性皮肤纤维肉瘤(DFSP)的超声表现。方法回顾性分析12例经手术病理证实的隆突性皮肤纤维肉瘤的分布、超声图像特征及彩色多普勒血流成像特点。结果12例隆突性皮肤纤维肉瘤患者中,11例(91.67%)为单发,直径0.9～8.0cm;分布在躯干66.67(8/12)、四肢近端16.67%(2/12)、头颈部16.67%(2/12);83.33%(10/12)肿瘤出现在躯干及四肢近端的皮肤与皮肤下层。91.67%(11/12)肿瘤呈不均匀弱回声,66.67%(8/12)边界清楚,形态规则,肿瘤内部无液化或钙化且不伴有局部淋巴结转移;91.67%(11/12)肿瘤内彩色多普勒显示有丰富彩色血流信号。结论患者躯干及四肢近端的皮肤与皮下层肿块,边界清楚、形态规则、内部呈不均匀弱回声、内部血流较丰富、无局部淋巴结肿大是隆突性皮肤纤维肉瘤的超声表现。

Objective To explore the ultrasonographic appearance of dermatofibrosarcoma protuberans. Methods Clinical data, sonographic features and color Doppler flow imaging characteristics of 12 patients surgically and pathologically con- firmed dermatofibrosarcoma protuberans were retrospectively analyzed. Results Single mass was detected in 11 patients （11/12, 91.67%） with the diameter ranged0.9--8.0 cm. The tumors distributed in the trunk （8/12, 66.67%）, proximal limbs （2/12, 16.67%） or face and neck （2/12, 16. 67%）. Most of the tumors （10/12, 83.33%） developed from skin and subcutaneous fat layer of the trunk and limbs and were hypoechoic and heterogeneous （11/12, 91.67%）, some （8/12, 66.67%） with distinct boundary and regular shape without liquification, calcification nor regional lymph node metastasis. Affluent color Doppler flow signals of tumor were found in 11 patients （91.67%）. Conclusion Ultrasonographic characteristics of dermatofibrosarcoma protuberans include distinct boundary, regular shape, heterogeneous hypoechogenicity and rich color Doppler flow signals without regional lymph node metastasis.