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Ⅵ型Ehlers-Danlos综合征合并肾动脉自发破裂及肾动脉-下腔静脉瘘形成一例 被引量:1

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摘要 患者男,32岁。因无诱因发生剧烈右腰区疼痛伴肉眼血尿2d于2006年11月7日急诊入院。既往幼年始皮肤易破损,其母亲与他特征相似。行常规检查后,初步判断为泌尿系疾病收入泌尿外科。入院后第2天发生充血性心力衰竭,呼吸困难,不能平卧。彩色超声检查排除了泌尿系结石疾病,发现与肾动脉和下腔静脉相连的巨大血肿转入血管外科。体格检查:脉搏91次/mim,血压130/90mmHg,
出处 《中华普通外科杂志》 CSCD 北大核心 2009年第9期771-771,共1页 Chinese Journal of General Surgery
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同被引文献18

  • 1Tanaka T, Hayakawa M, Sadato embolization for carotid-cavernous A. et al. Transvenous fistula in a patient with vascular type of Ehlers-Danlos syndrome--direct superior ophthalmic vein approach: case report [ J ]. Neurol Med Chir (Tokyo), 2014,54(2) :155-160.
  • 2Abayazeed A, Hayman E, Moghadanffalah M, et al. Vascular type Ehlers-Danlos Syndrome with fatal spontaneous rupture of a right common iliac artery dissection: case report and review of literature[J]. Radiology Case, 2014, 8(2) :63-69.
  • 3Wheeler SM, Russo M, Wilson-Murphy M, et al. Gynecologic and Surgical Complications in Type 1V Ehlers-Danlos Syndrome [J]. Obstet Gynecol, 2014,123(2 Pt 2 Suppl 2):431-433.
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  • 6Naing BT, Watanabe A, Tanigaki S, et al. Presymptomatic genetic analysis during pregnancy for vascular type Ehlers-Danlos syndrome[J], lnt Med Case Rep J, 2014,7:99-102.
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