儿童臀部韧带样瘤的手术治疗

Operative Management of Desmoid Tumors of Gluteal Region in Children

目的：报告１３例儿童臀部韧带样瘤的临床资料并讨论其手术治疗问题。方法：１３例均进行了手术处理。结果：肿瘤切除术后，９例随访１年至８年２个月（平均３年４个月），３例肿瘤复发。结论：韧带样瘤具有浸润性生长特点，局部切除后易复发，但不发生转移和恶变。应早期诊治。为防止肿瘤复发，应广泛切除受累的臀肌、韧带、骨膜、骨质。

Objective: To review our experience of management of desmoid tumors of gluteal region in children. Methods: Thirteen cases of desmoid tumors of gluteal region were studied retrospectively. Results: The tumors involved gluteus maximus(13), gluteus medius(11), gluteus minimus(6), tensor fasciae latae(4), piriformis(4), periostium of ilium(9), ilium bone(6) and sacro iliac joint(4). Seven patients had tumour extension into the pelvis cavity via greater sciatic notch. Post operatively, nine patients were followed up for a mean period of 3 years and four months (range:1 8 years). Tumour recurred in three patients. Conclusions: Desmoid tumors are locally invasive and prone to recur after excision. Malignant change is unlikely. Wide excision is advised to minimize recurrence.