先天性无阴道的诊治

Diagnosis and treatment of congenital absence of the vagina

先天性无阴道患者大多数为MRKH综合征,无阴道同时子宫缺如,表现原发性无月经或性交困难。本病应与阴道闭锁、雄激素不敏感综合征等鉴别。治疗可取保守顶压的Frank法,但多数手术行阴道成形术。当今,以开腹或腹腔镜行乙状结肠阴道成形术、腹膜阴道成形术或Vechietti阴道成形术等为主流手术。

Congenital absence of the vagina is usually associated with the Mayer-Rokitansky-Kuster-I-Iauser （MRKH） syndrome, which characterized by absence of vagina and uterus. Patients presenting with primary amenorrhea and dyspareunia should be distin- guished from other defects of genital tract development such as vaginal atresia and androgen insensitivity syndrome. Treatment could be surgical （vaginoplasty） and nonsurgical （ Frank＇s technique）. Currently, the most widely used remedies are laparotomy or laparoscopic Vecchietti procedure and vaginoplasty with sigmoid or peritoneum. Keywords：