视网膜耳蜗脑微血管病并突发周边视野缺损及听力损失:Susac综合征1例(英文)

Retinocochleocerebral microangiopathy with sudden peripheral visual field defects and hearing loss:a case of Susac-syndrome

目的:报告1例25岁女性患Susac综合征(SS),突发周边视野缺损及听力丧失。方法:报告1例25岁女性患者突发周边视野缺损及听力丧失,并记录视网膜超广角血管造影检查结果之间的相互关系以及所展现的视野缺损。结果:患者显现出SS特有的临床三联征。我们可以看出视网膜超广角血管造影检查结果和视野缺损之间的一些相互关系。结论:经证明超广角血管造影术是一个在临床治疗中检测和追踪SS周围病变的有价值的工具。

AIM： To report a case of Susac-syndrome （SS） in a 25 years old female with sudden peripheral visual field defects and hearing loss. METHODS： A 25 years old female with sudden peri- pheral visual field defects and hearing loss was reported, and the correlations between retinal findings in ultrawidefield-angiography and presented visual field defects were documented. RESULTS： Our patient presented the characteristic clinical triad of SS. Certain correlations between retinal findings in ultra-widefield-angiography and visual field defects could be shown. CONCLUSION： Ultra-widefield-angiography has been proven to be a valuable tool to detect and follow peripheral lesions of SS in clinical management.