肌萎缩侧索硬化的营养支持治疗与经皮内镜下胃造瘘
被引量:6
摘要
肌萎缩侧索硬化(amyotrophic lateral sclerosis,ALS)又称运动神经元病(motor neuron disease,MND),是一种致死性神经系统退行性疾病,由于上、下运动神经元变性导致延髓部、四肢、躯干、胸部及腹部肌肉逐渐无力和萎缩。该病隐袭起病,进展缓慢,多因肺部感染引起呼吸衰竭而死亡。发病率约1.5/10万,患病率(4~6)/10万。发病年龄平均55岁,发病起平均存活3.5年,5年后有20%患者存活。
出处
《中华神经科杂志》
CAS
CSCD
北大核心
2010年第2期139-141,共3页
Chinese Journal of Neurology
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