垂体性侏儒症伴第三脑室底鞍下扩展、双垂体畸形一例
被引量:2
摘要
患者女,19岁。因生长发育迟缓十余年而人我院内分泌科诊治。患者系7个月早产儿,顺产,出生体质量2150g。出生后1年内即发现生长发育落后于同龄儿童。12岁后身高停滞,无第二性征发育,双眼视灵敏度下降6年余。智力一般,奁体患者身高130cm,体质量35kg,面容幼稚,双乳部位少许脂肪堆积,外阴幼稚。MRI示鞍区囊状异常信号,第三脑室延长,并伸入蝶窦内,未见明短增强垂体信号。鞍膈鞍底缺如,前联合未见显示,蝶鞍两侧见垂体结构(图1a~d)。
出处
《中华神经外科杂志》
CSCD
北大核心
2010年第3期285-285,共1页
Chinese Journal of Neurosurgery
同被引文献32
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