颅内血管网状细胞瘤38例临床分析

Clinical Analysis of 38 Cases of Intracranial Hemangioblastomas

目的:分析颅内血管网状细胞瘤的临床特点。方法:对我院1975年～1996年收治并经病理证实的血管网状细胞瘤38例作一回顾性研究。结果:发病年龄多数为20～50岁,男性多于女性,绝大多数发生于小脑。26例行CT检查,肿瘤分囊性者23例,其中4例又作MRI检查,肿瘤为囊性者3例。瘤结节及实性肿瘤全切除36例,部分切除加放射治疗2例。结论:MRI检查对囊性血管网状细胞瘤的诊断有特异性;手术切除程度和病变呈多灶性与肿瘤复发有关;肿瘤具有明显的遗传倾向。

Objective:To analyse the clinical features of intracranial hemangioblastomas. Methods: 38 cases of intracranial hemangioblastomas confirmed by pathological examination were studied retrospactively from 1975 to 1996. Results: Tumors occured chiefly in patients between 20 and 50 years of age and more often in men than women. The most of tumors located in the posterior fossa of cerebellum.Twenty six were performed CT scanning, in which 4 cases were examined by magnetic resonance imaging (MRI). Musal nodules and solid masses were completely resected in 36 tumors and subtotal removal and received radiotherapy in remaine 2 cases. Conclusion: MRI has more specificity in diagnosis of cystic hemangioblastomas.The degree of resection and multiple focuses of tumor could influence the recurrence rate of hemangioblastomas; and which has obvious inheritance tendency.