成人真两性畸形1例报告并文献复习

one Cases Report of True Hermaphroditism in Adult and the Literature Review

目的:提高对真两性畸形的诊疗经验。方法:对深圳市坪山人民医院收治的1例真两性畸形患者临床资料结合文献复习回顾性分析。结果:本患者社会性别女性,女性第二性征明显,手术探查并切除体内睾丸组织,恢复良好。随访1a,性激素水平正常。结论:真两性畸形确诊依靠影像学、细胞遗传学、性腺组织病理学等检查,治疗原则为切除与决定性别相抵触的性腺,并行相应外生殖器矫形术,以恢复性功能为目的。

Objective：Improve the diagnosis and treatment of true hermaphroditism.Methods：One true hermaphroditism case in our hospital was analyzed retrospectively,and then review of the literature.Results：The female patient had obvious female secondary sexual characteristics,after the explorative operation and Removal of testis,the body was primly recuperated.1 year follow-up later,the level of sex hormone is normal.Conclusions：The accurate diagnosis of true hermaphroditism should be made on radiology,cytogenetics and histological examination of the gonad.The principia of treatment included the removal of the contradictory gonad and the genitalia orthopedics.The purpose of diagnoses and treatment was to recover sexual function.