烟雾病的磁共振表现

The appearance of Moyamoya disease on magnetic resonance

目的分析烟雾病的磁共振成像(magnetic resonance imaging,MRI)及磁共振血管造影(magnetic resonance angiography,MRA)表现,探讨柔脑膜高信号(IVY征)对烟雾病的诊断价值。方法回顾分析10例确诊为烟雾病患者的临床及MR资料。结果MRI上分别可以出现双侧大脑前动脉、大脑中动脉的异常,双侧基底节区出现血管流空信号影,IVY征,梗塞灶。MRA表现为双侧颈内动脉末端及大脑前、中动脉的狭窄或闭塞;大脑后动脉增粗延长;烟雾血管。结论烟雾病的MR诊断要点为:双侧颈内动脉末端及大脑前、中动脉的狭窄或闭塞;烟雾状侧支血管的存在。其中IVY征是侧支血管的表现,其对烟雾病的诊断价值应引起重视。

Objective To analyze the appearance of Moyamoya disease on magnetic resonance imaging（MRI） and magnetic resonance angiography（MRA）,to approach the value of high signal leptomeninges to Moyamoya disease.Methods The clinic and magnetic resonance data from 10 cases were analyzed.Results On MRI,complete bilateralis anterior and middle cerebral artery couldn＇t be seen;Moyamoya vessels in the basal ganglia,leptomeningeal high signal intensities and ischemia could be displayed.On MRA,stenosis or conclusion of the distal internal carotid,anterior and middle cerebral artery were revealed;thickening and extending posterior cerebral artery was showed;Moyamoya vessles could be displayed.Conclusion There are two main diagnostic points of Moyamoya disease on MR,and leptomeningeal high signal intensities has important meaning to diagnose Moyamoya disease.