空肠血管外皮瘤1例报道

Hemangioperictytoma of jejunum:one case report

空肠血管外皮瘤多发生于青年人,可发生于身体的任何部位,空肠血管外皮瘤发病率很低,临床表现多为无痛性肿块。病理学检查可见肿瘤实质内有丰富的薄壁血管,其相互连接成网状、树枝状或鹿角状。瘤细胞排列密集,可见核分裂。网状纤维染色瘤细胞位于血管外,包绕单个瘤细胞。免疫组化Vimentin(+),少数病例Desmin可散在阳性。空肠血管外皮瘤生物特性多样,恶性程度差别很大,根治性切除是治疗血管外皮瘤的有效方法。恶性血管外皮瘤可发生远处转移,放化疗尚无确切疗效。

Hemangioperictytoma（HPC） of jejunum is more common in young people and could occur at any part of the body.HPC is a very rare tumor in gastrointestinal tumor,mostly painless mass in clinical.There are tightly packed cells growing around ramifying,thin-walled,endothelium-lined vascular channels ranging from larger sinusoidal spaces to small capillaries microscopically.Vimentin（＋） of immunohistochemistry is the diagnosis of HPC.The degrees of malignancy vary widely of HPC,radical resection is the effective treatment for HPC.Metastasis of malignant HPC may occur.There is not therapeutic effect in radiotherapy and chemotherapy.