摘要
Extrarenal Wilms' tumour(ERWT) is extremely rare with a scant mention in the literature.We described a 7 yearold girl who presented with abdominal pain,vomiting and constipation.Diagnostic investigation and exploratory laparotomy provided evidence of a huge retroperitoneal mass in the lumbosacral area with normal kidneys.Histology and immunophenotyping confirmed the diagnosis of Wilms' tumour.Bone marrow revealed infiltration with non-hematogenous cells and patient was started on chemoradiotherapy.Presently patient is on our follow up and asymptomatic for her disease.
Extrarenal Wilms＇ tumour（ERWT） is extremely rare with a scant mention in the literature.We described a 7 yearold girl who presented with abdominal pain,vomiting and constipation.Diagnostic investigation and exploratory laparotomy provided evidence of a huge retroperitoneal mass in the lumbosacral area with normal kidneys.Histology and immunophenotyping confirmed the diagnosis of Wilms＇ tumour.Bone marrow revealed infiltration with non-hematogenous cells and patient was started on chemoradiotherapy.Presently patient is on our follow up and asymptomatic for her disease.
