摘要
目的总结颅内非典型畸胎瘤样-横纹肌样瘤(atypical teratoid-rhabdoid,AT-RT)的诊治经验。方法回顾性分析3例诊断为颅内AT-RT病人的临床资料,其中儿童2例,成人1例,总结其临床特点、神经影像学特点、手术治疗及预后。结果肿瘤全切除2例,近全切1例。术后放疗2例,随访6～13个月,3例病人目前均存活。结论颅内AT-RT是罕见的高度恶性肿瘤,总体预后较差,手术是本病主要的治疗手段。
Objective To review the experiences in diagnosis and treatment of intracranial atypical teratoid-rhabdoid tumor （AT-RT）. Methods Clinical data of 3 patients,two children and 1 adult,with intracranial AT-RT,including the clinical features,neuroimaging characteristics,treatment and prognosis,were analyzed retrospectively. Results Total tumor resection was achieved in 2 patients and subtotal removal in 1. Two patients received postoperative radiotherapy. The follow-up was performed from 6 to 13 months with all the patients alive at present. Conclusions Intracranial AT-RT is a rare and highly malignant tumor with poor overall prognosis poor,and surgery is the main treatment method.
出处
《中国微侵袭神经外科杂志》
CAS
北大核心
2010年第5期205-208,共4页
Chinese Journal of Minimally Invasive Neurosurgery
