脑裂畸形的CT表现特征分析

Analysis on the CT finding features of Schizencephaly

目的探讨脑裂畸形的CT表现特征及其诊断价值。方法回顾性分析20例脑裂畸形的CT资料。男12例,女8例;年龄10个月至39岁,其中10岁以下14例,11～39岁6例。结果 CT特征性表现为病侧大脑半球内自皮质到侧脑室的横跨裂隙,裂隙两旁为内折的灰质。裂隙内端多数为有侧室外壁的憩室状突起,外端脑表面开口处均有楔形或扇形扩大。所称灰质与大脑皮层连续,与皮质呈等密度。单侧型14例,双侧型6例,共有26个裂隙,闭合型(Ⅰ)脑裂21个,开放型(Ⅱ)脑裂5个。合并其它脑先天畸形15例。结论脑裂畸形的CT表现具有特征性,能良好显示脑裂畸形的病理解剖特征。

Objective To explore the CT imaging features of schizencephaly and its diagnostic value. Methods CT findings of 20 cases of schizencephaly were analyzed retrospectively, among them there were 12 male patients and 8 female patients, the aged from 10 months to 39 years, fourteen patients were under the age of 10 years and the remained 6 patients were in the age of 11-40 years. Results The characteristic CT finding of the disease was a transcerebral fissure extending from pial surface of the involved brain to the lateral ventricle. The fissure was lined by rolling in gray matter. Enlargements of both ends of clefts which appeared as fan-shaped or wedge shape at their lateral ends and as diverticulum from lateral ventricles at their ventricular ends, were noted in above cases. Lined gray matter, which was isodensity on CT, was continuous with adjacent cortices. There were unilateral clefts in 14 cases and bilateral in 6 cases. Totally there were 26 clefts, among them 21 were closed （Type Ⅰ ）, and 5 were open （Type Ⅱ）. Accompanying congenital brain malformations were found in 15 cases. Conclusion For its typical and characteristic appearance, CT can display the pathological and anatomical feature of schizencephaly.