肝血管平滑肌脂肪瘤23例诊治分析

Retrospective analysis of 23 hepatic angiomyolipoma

为了探讨肝血管平滑肌脂肪瘤(HAML)的诊断和治疗方法,对经病理确诊的23例HAML的临床资料进行回顾性分析。23例患者中无特异症状16例,右上腹不适7例。肝功能无异常,AFP均为阴性。术前影像学诊断准确率21.7%。23例患者均接受手术治疗,1例死于术后心功能衰竭,其余22例随访无复发。初步研究结果提示,HAML的术前诊断困难,肿瘤内脂肪成分为脂瘤型HAML的特征性表现。手术切除是主要治疗方式。

The objective of this study was to explore the diagnosis and treatment of hepatic angiomyolipoma（HAML）.A total of 23 HAML patients confirmed pathologically were treated.Their clinical records were retrospectively analyzed.Of the 23 patients,16 were asymptomatic and 7 presented with right upper quadrant pain.Alpha fetoprotein（AFP）was negative in all the patients.The correct diagnostic rate was 21.7% preoperatively.Surgical treatment were performed in all 23 patients.One patient died of postoperative heart failure and the other 22 had no recurrence during follow up.HAML is difficult to be diagnosed preoperatively.Fatty content within the tumor is the characteristic of lipoma-type HAML.Surgical resection is the mainstay of the treatment of HAML.