肝血管平滑肌脂肪瘤13例报告

Hepatic angiomyolipoma., a report of 13 cases

目的探讨肝血管平滑肌脂肪瘤的临床表现和预后。方法回顾性分析经手术治疗的13例肝血管平滑肌脂肪瘤病人的临床资料。结果该肿瘤缺乏特征性临床症状，影像学表现多样，术前仅1例诊断肝脏血管平滑肌脂肪瘤。病理诊断需依赖标本免疫组化指标HMB45阳性。结论该肿瘤术前容易误诊，首选手术治疗，预后良好。

Objective To investigate the clinical features and prognosis of hepatic angiomyolipoma（HAML）. Methods Clinical data of 13 patients with operatively confirmed HAML treated in our hospital were retrospectively analyzed. Results HAML was usually asymptornatic and the imaging features varied. Only 1 case was correctly diagnosed before operation. HMB45 positive staining was the pathologic characteristic of HAML. Conclusion HAML can be easily misdiagnosed, should be properly treated by surgery and has a good prognosis.