原发性肺动脉肉瘤——附一例报告

Primary sarcoma of pulmonary artery: a case report

目的提高对原发性肺动脉肉瘤的认识。方法通过一肺动脉肉瘤病例，详细分析此类疾病的临床症状、放射学特征及病理表现。结果本病与其他肺动脉阻塞性疾病（包括肺血栓栓塞）的临床表现并无明显差异。对疑为肺血栓栓塞的病人，当放射影像学出现单侧肺动脉扩张、持续性软组织充盈的肺动脉、肺内肿块，临床呈现经抗凝和溶栓治疗后病情依然恶化等情况时，均高度提示本病。结论肺动脉肉瘤极易误诊为其他肺血管阻塞性病变，应予重视。

Objective To call attention to the rare involvement of pulmonary artery by sarcoma. Methods To summarize the clinical, radiological and pathologic features of a case of pulmonary artery sarcoma. Results Pulmonary artery sarcoma has similar clinical manifestations as other pulmonary artery obstructive diseases (including pulmonary thromboembolism). The diagnosis should be considered in the patient with clinical presentations suggested pulmonary embolism. The radiological findings included unilateral hilar enlargement, contiguously soft tissue filled pulmonary artery and pulmonary nodules and clinically deterioration was found after anticoagulant therapy. Conclusion Pulmonary artery sarcoma is usually misdiagnosed as other pulmonary artery obstructive diseases. More attention should be paid to it.