儿童先天性肺囊腺瘤样畸形的影像诊断

Diagnostic imaging of children's congenital cystic adenomatoid lung malformation

目的:描述儿童先天性肺囊腺瘤样畸形的影像特点,提高对该病的认识。方法:对我院1998～2010年14例儿童先天性肺囊腺瘤样畸形患者的临床资料进行分析。结果:经胸片检查发现,见单个或多个含气大囊7例,见多发蜂窝样小囊5例,肿块样改变2例,其中合并肺纵隔疝9例,出现患侧肺气肿10例;经CT检查发现,右肺受累6例,左肺受累8例,其中表现为巨大囊腔5例,类圆形薄壁囊腔3例,蜂窝样小囊5例,含有少量液体3例;病理检查,囊腔壁有异常增生6例。结论:影像学检查是诊断儿童先天性肺囊腺瘤样畸形的可靠方法。

Objective： To investigate the imaging features of children＇s congenital cystic adenomatoid lung malformation,and improve knowledge of the disease.Methods： The clinical data of 14 patients with children＇s congenital cystic adenomatoid lung malformation from 1998 to 2010 in our hospital were analyzed.Results： Chest X-ray inspection,7 patients had single or multiple large cyst containing gas,5 patients had multiple honey combing-like vesicles,2 patients had tumor-like pathological changes,9 patients incorporated with pulmonary mediastinal hernia,and 10 patients with emphysema at the affected side;CT examination,right lung was implicated in 6 patients,left lung was implicated in 8 patients,and 5 patients incorporated with large cysts,3 patients had circular thin-walled cystic lesion,5 patients had honey combing-like vesicles,3 patients had a few liquid;pathologic finding： 6 patients incorporated with atypical hyperplasia at cavity wall.Conclusion： Imaging findings is a reliable method in order to diagnose children＇s congenital cystic adenomatoid lung malformation.