色素性隆突性皮肤纤维肉瘤

A case of pigmented dermatofibrosarcoma protuberans

报告1例色素性隆突性皮肤纤维肉瘤患者。患者男,30岁。左上臂蓝色斑块半年就诊。皮肤科检查:左上臂三角肌处一蓝红色斑块,表面轻微萎缩凹陷。皮损组织病理检查:真皮内有一瘤细胞团块,细胞核呈梭形,核大、深染,无明显异形,排列成车辐状或条索状,含黑素的树突状细胞不规则分布于瘤细胞之间。免疫组化染色示CD34(+),波形蛋白(vime ntin)(+)。诊断为色素性隆突性皮肤纤维肉瘤。

A case of pigmented dermatofibrosarcoma protuberans is reported. The patient was male, 30 years old. He had blue plaque on the left upper arm for nearly half a year. Examination showed a blue-red plaque on the deltoid of left upper arm, slight atrophy and depression in the surface, with the plaque reached subcutaneous. Histopathological examination showed tumor cell mass in the dermis. Spindle--shaped nucleus, large, deep--dyed, non-atypia, arranged as spoke or cord. The pigmented dendritic cells randomly distributed among the whole tumor cells. Immunohistochemical stain showed CD34 and vimentin were positive. Diagnosis of pigmented dermatofi- brosarcoma protuberans was made.