先天性巨输尿管症(附10例报告)

Congenital megaureter(Report 10 Cases)

目的：探讨手术治疗先天性巨输尿管症的时机和有效性。方法：总结本病１０ 例，其中男６ 例，女４ 例；儿童４ 例，成人６ 例；左侧４ 例，右侧２ 例，双侧４ 例。保守治疗１ 例；手术治疗９ 例，包括输尿管剪裁整形再植术 ５ 例，肾输尿管全切术４ 例。结果：９ 例获随访 ３ 个月～６ 年。４ 例患儿发育正常，健肾代偿性增大。双侧者术侧肾、输尿管积水减轻，症状明显缓解，保守侧无显著变化。结论：儿童患者应尽早手术治疗，成人患者可根据病变情况采用保守或手术治疗。

Purpose:To study the timing and efficacy of the surgery for the treatment of congenital megaureter.Methods:Between May 1986 and Jan 1998,10 patients with congenital megaureter were treated.Among them,6 cases are male and 4 female,4 children and 6 adults,left side 4 cases,right side 2 and bilateral 4. Surgical route was adopted in 9 patients,in which 5 cases underwent ureteroplasty reimplantation;4 cases nephroureterectomy,and 1 patient was given a long term observation.Results:All 9 petients were followed up from 3 months to 6 years.4 children had a normal growth.There were enlargement in their remained healthy kidneys.They were found that the hydronephrosis and hydroureter of the operated side of the patients with bilateral disorder had reduced and the symptoms of the patients with bilateral disorder had reduced and the symptoms of the patients relieved.There were no significant change on the none operated side.Conclusions:The children patients should receive surgical treatment earlier.The adult patients can be viewed or receive surgical treatment if nesessary.