蝶骨平台巨大颅骨混合型血管瘤1例报告并文献复习

Huge mixed hemangioma in planum sphenoidale:a case report and literature review

目的探讨蝶骨平台颅骨混合型血管瘤的临床特征和预后。方法报告1例蝶骨平台巨大混合型血管瘤,结合相关文献分析其临床、影像学及病理特点,探讨其诊断、治疗及预后。结果原发颅骨内血管瘤临床比较少见,约占颅骨肿瘤的0.7%,发生在颅底罕见。X线检查可见颅骨内蜂窝状改变,CT、MRI显示颅骨溶骨性病变并向颅内外发展,DSA造影病变常无明显染色,病理显示大小不等的异常血管、骨结构异常以及出血征象。外科治疗为首选。结论颅骨血管瘤为颅骨内破坏性病变,单发性手术疗效好,但多发性欠佳。

Objective To study dinical feature and prognosis of the mixed hemangioma in planum sphenoidale.Methods The imaging feathures of the CT,MRI were analysed in a patient with huge hemangioma.The radiological and pathologic findings were reviewed in the literatures to hemangioma of the skull.Results The calrarical hemangioma is an uncommon tumor,accounting for 0.7% of the skull.Most of the tumors are singularly found.all the calvarium appeared hongycomb-like on the skull X-film in the patient with calvarial hemangioma.The CT and MRI showed that the calvarium had ostedytic lesion or erosion and the tumor grew intracranially and extracranially.The DSA revealed that the tumor was not stained.The pathological examination showed the abnormal blood vessels.The disorder bone structure and haemorrhage were seen.Conclusion The hemangioma of the skull was a destructive disease.The curative effect of the operation on the calvarial hemangioma involving all the skull is bad.