成人原发性肾肉瘤

Primary renal sarcoma in adults

目的 探讨成人原发性肾肉瘤的诊断、治疗及预后。 方法 １９８５ ～１９９５ 年共收治肾脏肿瘤３５３ 例，其中成人原发性肾肉瘤７ 例，占１９ ％ 。采用回顾性研究。 结果 ７ 例均行外科手术治疗。术后病理确诊平滑肌肉瘤３ 例、横纹肌肉瘤２ 例、梭形细胞肉瘤１ 例、低分化肉瘤１ 例。术中死亡１ 例。术后随访３ ～６０ 个月，平均生存１４ 个月。 结论 成人原发性肾肉瘤高度恶性，以平滑肌肉瘤最常见。早期诊断和外科手术切除是目前唯一提高疗效的方法，但总体预后较差。

Objective To review 7 cases of renal sarcoma in adults and to present the diagnosis,treatment and prognosis. Methods From 1985 to 1995,7 cases of renal sarcoma in adults out of 353 cases of renal neoplasms (1.9%) were treated.The 7 cases were reviewed. Results All the 7 cases were confirmed on pathological studies,consisting of 3 leiomyosarcoma,2 liposarcoma,1 spindle cell sarcoma and the other 1 not specified.Radical nephrectomy was conducted for all with 1 short term mortality.The others survived for a mean of 14 months. Conclusions Renal sarcoma was more common in female,pain and a palpable mass being the most common presenting complaints.The tumors were bigger than 10cm.On CT and MRI cystic mass with solid components could be observed.Surgical ablation is the only means of treatment yet the prognosis is poor.