先天性迷走左肺动脉5例报告并文献复习

Congenital aberrant left pulmonary artery:5 cases report and review of the literature

目的:总结先天性迷走左肺动脉(CALPA)的诊断和治疗方法。方法:总结2009年4月至2010年3月确诊CALPA的5例患儿的临床表现、诊断和手术方法。结果:所有患儿均经超声心动图及螺旋CT确诊,2例保守治疗缓解。手术治疗3例,1例死亡;另2例分别为术后1 w和11个月,目前均情况良好。结论:婴儿早期出现反复喘息、肺部感染及气道梗阻表现时,应考虑CALPA的可能。超声心动图、螺旋CT是确诊的最佳方法。一旦确诊须尽快手术,手术重点包括左肺动脉移植术及气管成形术。

Objective：To Study of the diagnosis and treatment of congenital aberrant left pulmonary artery（CALPA） by reviewing the clinical and radiological data.Methods：Between April 2009 and March 2010,5 patients affected by congenital CALPA were admitted in our hospita1.The clinical features,Diagnostic means and surgical treatment methods of CALPA were discussed.Results：CALPA was found in all patients by echocar-diograph and spiral CT.Two patients got better by expectant treatment.Three patients were surgically treated,These procedures resulted in one learly death,Another 2 patients are doing wel1 now.Conclusion：Repeatedly wheezing,lung infection and airway obstruction manifestations in early infancy should consider CALPA.Echocardiography and spiral CT is the best methods to the diagnosis of CALPA.Surgical interfering should be done as soon as diagnose is made.The surgical techniques include left pulmonary artery reimplantation and tracheo-plasty.