儿童线粒体脑肌病14例临床观察及护理

Clinical observation and nursing care of 14 children patients with mitochondrial encephalomyopathy

目的:观察线粒体脑肌病患儿的临床表现,进行相应的护理干预。方法:对14例患儿针对主要临床表现进行对症护理,包括抽搐、头痛、呕吐、意识障碍,针对患儿的情绪障碍、自伤倾向、认知障碍进行针对性护理,并对患儿家长进行健康教育、心理护理、康复训练指导。结果:经精心护理,患儿均未发生护理并发症,患儿家长能够保持平和心态,积极参与对患儿的照护。结论:儿童线粒体脑肌病临床表现复杂多样,护理难度大,积极、有效的护理干预是该病治疗成功的保障。

Objective： To observe the clinical manifestations of children patients with mitochondrial encephalomyopathy and conduct appropriate nursing intervention.Methods： The symptomatic nursing care was given to 14 children patients according to their clinical manifestations,such as convulsion,headache,vomiting and disturbance of consciousness.Meanwhile the targeted nursing care was applied to the patients in allusion to their mood disorders,tendency to self-injury and cognitive impairment.The parents of the children patients were given health education and guidance on psychological care and rehabilitation coaching.Results： After careful nursing care,no complications due to nursing care occurred in any children patient;the parents could keep a calm mind and actively participated in their children＇s care.Conclusions： The nursing care is very difficult because of the complex and varied clinical manifestations of mitochondrial encephalomyopathy,so positive and effective nursing intervention is the key to successful treatment of the disease.