Marfan综合征晶状体半脱位一家系的手术疗效观察

Effects of surgical treatment on subluxation of lens in marfan syndrome in a family

目的探讨Marfan综合征晶状体半脱位患者的手术疗效。方法对一家系4例(6只眼)Marfan综合征晶状体半脱位患者进行手术治疗,1例(1只眼)行白内障超声乳化吸除、囊袋张力环、人工晶状体植入术,另3例(5只眼)行白内障超声乳化吸除、后房型悬吊人工晶状体缝合术。结果术后3个月6只眼的视力均有不同程度的提高;5只眼人工晶状体的位置居中,1只眼人工晶状体的位置发生偏移,经调整后位置正常;均未见暴发性脉络膜上腔出血、视网膜脱离等严重并发症。结论对于Marfan综合征晶状体半脱位的患者,应掌握好手术适应证,选择合适的手术方法以确保手术成功。

Objective To discuss the effects of surgical treatment on subluxation of lens in Marfan syndrome. Methods Surgical treatment was performed on four cases （six eyes） with subluxation of lens in Marfan syndrome in a fam- ily： One （one eye） with phaccemulsification cataract and intmocular lens implantation with capsular tension, the three oth- er patients （five eyes）with phacoemulsification cataract and implantation of a posterior chamber intraocnlar lens. Results Visual acuity of all six eyes was improved in three months after the surgery. Intraocular lens position of five eyes was per- fectly in center; only one shifted and back to normal position after surgical adjustment. No severe complications, such as expulsive haemorrhage or retinal detachment , occurred. Conclusion For patients with subluxation of lens in marfan syn- drome, doctors should select good surgical indications and appropriate surgical method to improve the successful rate.