特殊类型的嗜铬细胞瘤

Atypical pheochromocytoma

目的 提高对特殊类型嗜铬细胞瘤的诊断及治疗水平。 方法 总结１９８５ 年７ 月至１９９８ 年８ 月期间收治的嗜铬细胞瘤５１ 例。 结果 ５１ 例中１９ 例病情较为特殊，主要表现为静止功能、双侧发病、异位、恶性表现、复发及合并妊娠。针对不同的嗜铬细胞瘤类型采用不同的围手术期治疗方法全部切除肿瘤。随访６ 个月～９ 年，除复发病例外，血压基本恢复正常。 结论 充分的围手术期治疗是确保手术成功的关键。

Objective To improve the diagnosis and treatment of atypical pheochromocytoma. Methods 51 cases of pheochromocytoma were treated from July 1985 to August 1998. Results Of the 51 cases, 19 were atypical, and were characterized by silient tumor, pheochromocytoma in pregnency, bilateral tumor, extraadrenal tumor, malignant tumor, and recurrent tumor. Open operation was performed for all kinds of cases in accordance with their special characteristics. Conclusions Surgical extirpation is the only means for the treatment of atypical pheochromocytoma and meticulous perioperative management is essential.