原发性肺动脉肉瘤1例并文献复习

A case of primary pulmonary artery sarcoma and literature review

目的提高对原发性肺动脉肉瘤的认识和诊断水平。方法结合我院l例经手术病理证实的原发性肺动脉肉瘤患者的临床资料与国内外有关文献，对原发性肺动脉肉瘤的临床表现、影像学表现、实验室检查结果进行分析。结果原发性肺动脉肉瘤的临床表现与肺动脉血栓栓塞相似，应用CT肺动脉造影鉴别有一定局限性，正电子发射型计算机断层扫描与CT合用有助于诊断。结论原发性肺动脉肉瘤临床表现及常规影像特异性较少，正电子发射型计算机断层扫描与CT结合有更大的诊断价值。

Objective To improve the understanding of primary pulmonary artery sarcoma（PAS） and raise the level of diagnosis. Methods The clinical manifestations, imaging manifestation and laboratory tests of PAS were analysed combined with the clinical data of one PAS patient confirmed with biopsy and relevant foreign and domestic literatures. Results The clinical manifestations of PAS are familiar to those of pulmonary thromboembolism （PTE）. There are certain limitations to identify PAS and PTE by CT pulmonary angiography and it is contributing to PET/CT. Conclusions The clinical manifestations and conventional imaging of PAS are less specific,and PET/CT is of more value.