脑裂畸形的CT、MRI诊断

CT/MRI Diagnosis of Schizencephaly

目的分析脑裂畸形的CT、MRI特点,提高其诊断准确性。材料与方法回顾分析13例CT、MRI发现的脑裂畸形影的像资料,男8例,女5例,年龄6天-56岁,平均25.3岁。CT检查10例,MRI检查4例,CT+MRI检查3例。结果本组13例均为单侧单条脑裂畸形,其中分裂型脑裂畸形5条(29.4%),融合型脑裂畸形8条(70.6%)。CT、MRI特点为大脑内出现横贯性裂隙即软脑膜-室管膜缝(piamater-ependyma缝,p-e缝),其壁由灰质构成,内侧端与侧脑室外侧壁相连,局部呈憩室样缺损;外侧端与软脑膜相连,局部蛛网膜下腔喇叭样或囊肿样增宽。结论 CT、MRI能清晰显示脑裂畸形的形态特征及其伴发畸形。

Objective To analyses the CT and MRI imagine features of schizencephaly and to improve its diagnostic accuracy.Material and methods 13cases of schizencephaly examined by CT and MRI were analyzed retrospectively.Of which,8 cases were males,5 cases were females.Age extended from 6 days to 56 years,mean 25.3 years.10 cases underwent CT scanning,4 cases underwent MRI scanning,3cases underwent CT and MRI scanning.Results In this series of schizencephaly,13 cases were all unilateral single form,of which 5 cases of schizencephaly were belonging to the open type,which was frequently happened 29.4%（5/13）,8 cases of schizencephaly were belonging to the colesed type,which was frequently happened 70.6%（8/13）.The characteristic CT and MRI findings was a trans-cerebral cleft namely piamater-ependyma sewing,which was lined by a gray matter.The medial side of cleft was connected by the diverticulum defect of lateral ventricle wall;The outside side of the cleft was connected by the trumpet or cyst-shaped of subarachnoid.Conclusion The pathology features of schizencephaly and its accompanying deformity can be clearly displayed by CT and MRI.