Ebstein心脏畸形的外科治疗

Surgical Treatment of Ebstein Anomaly

我所自1989年11月至1993年7月为5例Ebstein心脏畸形病人施行了外科治疗。其中3例行房化右心室游离壁折叠术和后瓣环成形术；1例行后瓣环成形术和手术切断旁路传导束及冷冻切断房室结双径路；1例行三尖瓣置换术。无术后早或晚期死亡。对手术适应证，认为手术时机可放宽到心功能严重受损以前施行。手术方法则应根据病变而选择。

Ebstein anomaly is an uncommon congenital cardiac malformation.From Nov.1989 to July.1993,5 patients with Ebstein anomaly were treated surgically.Of 5 patients（3 males and 2 females）,3 patients underwent the atrialized portion of the right ventricle and valvuloplasty;l patient received valvuloplasty with cutting of accessory pathway and cryoablation of AV node reentrant circuit and 1 patient had replacement of tricuspid valve.There was no early and late death after procedure.The patients were followed up for 3 to 47 months and they all recovered well.The authors believe that the timing of operation for Ebstein anomaly could be any time before the appearance of serious cardiac failure.In cases with cyanosis or other cardiac anomaly,the operation could be indicated even the patients cardiac function is in classⅡ(NYHA).The method of operation depends on the pathological lesion.