肺淋巴管肌瘤病的高分辨率CT表现

HRCT of Pulmonary Lymphangiomyomatosis

目的 通过总结肺淋巴管肌瘤病的ＨＲＣＴ 表现，讨论其诊断和鉴别诊断。方法 ３ 例均为女性，年龄为２４、２８ 和６９ 岁，其中６９ 岁患者合并右下肺腺癌。ＨＲＣＴ 扫描技术包括１－５ｍ ｍ 层面，骨重建算法，１４０ｋＶＰ和１４０ ～１７０ｍＡ。结果 ＨＲＣＴ均呈两肺多发，边缘清楚的薄壁囊状影，直径几毫米至２ｃｍ ，囊壁从隐约可见至１ｍ ｍ 厚，这些囊状影无外周或中心，上肺或下肺分布差异。１ 例可见双侧胸水，另１ 例除囊状影外右下肺可见直径３ｃｍ 的肿块。

Objective To describe the HRCT findings of lymphangiomyomatosis and discuss the diagnosis and differential diagnosis of this disease. Methods Three patients were all women. The ages were 24,28 and 69 years old. The oldest patient was proved by surgery with lymphangiomyomatosis and right lower lobe adenocarcinoma. The technique of HRCT scans of chest included 1.5mm collimation,bone algorithm reconstruction,140kVP and 140～170mA. Results HRCT scans showed multiple,well defined and thin walled cysts imaging in all three cases. The cystic air spaces ranged in diameter from a few millimeter to 2 cm. The walls of cysts range being faintly perceptible to near 1mm in thickness. There was no peripheral/central or upper lobe/lower lobe preponderance of the cysts. Bilateral pleural effusions were present in one case. A lung mass was showed in one patient. Conclusion HRCT is valuable in diagnosis and differential diagnosis of pulmonary lymphangiomyomatosis. [