巨大先天性海绵状淋巴管瘤

Giant congenital cavernous lymphangioma:a case report and literature review

报告1例巨大先天性海绵状淋巴管瘤。患儿男,14岁。临床表现为左大腿及左臀部巨大疣状斑块,曾于1岁时行手术切除,效果欠佳,术后手术切口处均出现散在囊性结节状新生物,且逐渐增大融合。磁共振成像(MRI)检查示软组织内广泛异常信号病变,考虑脉管瘤可能;皮损组织病理学检查显示真皮浅层淋巴管扩张,倾向于淋巴管瘤。结合国内外文献对淋巴管瘤的病因和检查,该例患儿诊断为巨大先天性海绵状淋巴管瘤。

A case of giant congenital cavernous lymphangioma is reported. A 14-year-old male presented with giant verru- cous plaque in his left thigh and left hip. An excision was performed when he was 1-year-old, but the result was unsatis-fied. Scattered postoperative cystic nodular neoplasm appeared in previous incision site, gradually enlarged and merged. Magnetic resonance imaging （MRI） showed widely anomalous signals in the soft tissue of lesions, suggesting vascular tumor. Histological examination showed numerous dilated lymphatic vessels in superficial dermis, prone to lymphangioma. According to domestic and foreign literatures, this case is diagnosed as giant congenital cavernous lymphangioma.