颅内原发性纤维黄色瘤1例报告并文献复习

Intracranial primary fibroxanthoma:a case report and literature review

目的总结颅内原发性纤维黄色瘤的诊治经验。方法回顾性分析1例经左侧额颞入路手术切除的颅内原发性纤维黄色瘤病人的临床资料,结合文献复习总结其诊断、治疗及预后。结果手术全切肿瘤,病理结果为脑膜起源的纤维黄色瘤。随访3个月,头颅MRI提示无肿瘤复发。结论颅内原发性纤维黄色瘤罕见,病理学是目前惟一可靠的诊断方法,首选手术治疗,早期诊断及全切肿瘤对于本病的预后意义重大。

Objective To review the experiences in diagnosis and treatment of intracranial primary fibroxanthoma.Methods Clinical data of one patient with intracranial primary fibroxanthoma was analyzed retrospectively,who was treated by surgery via left frontal-temporal approach.The diagnosis,treatment and prognosis were reviewed combined with literature analysis.Results The complete resection was achieved and the pathology diagnosis of the tumor was fibroxanthoma originating from meninges.The patient was followed up for 3 months and MRI showed no sign of recurrence.Conclusions Intracranial primary fibroxanthoma is rare,and pathological examination is the only reliable diagnosis method at present and surgical treatment is the first choice.Early diagnosis and complete resection of the tumor are very significant for the prognosis.