骨膜增生厚皮症

A case of pachydermoperiostosis

报告1例骨膜增生厚皮症。患者男,25岁。头面部皮肤及四肢末端进行性增生肥厚10年余。皮肤科检查:颜面部皮肤肥厚增生,折叠,呈沟回状,皮脂溢出明显,面容为痛苦绝望表情,眼距宽、鼻梁低、鼻端大,呈狮面,枕部头皮呈脑回样,皱襞粗大,沟嵴明显,前臂和小腿呈圆柱状,似象皮腿,手指和足趾呈杵状,小鱼际肥厚明显,呈铲样手,余检查未见异常。

A case of pachydermoperiostosis is reported. A 25-year-old man complained of progressive hyperplasia and hy- pertrophy skin of the face, head and distal parts of extremities for nearly 10 years. The patient showed a complexion of weariness and despair. The facial skin was thickened with furrows, folds and seborrhea. He had a striking feature, presented as ocular hypertelorism, low nasal bridge, big nose and leonine facies. The occipital scalp was thickened and showed cutis vcrticis gyrata. The forearms and legs were in the shape of cylinder, like elephantiasis. The fingers and toes were club- shaped with a ＂spade-like＂ appearance, and the hypothenar eminences enlarged.