腹外型侵袭性纤维瘤病的CT表现

CT features of extra-abdominal aggressive fibromatosis

目的:探讨腹外型侵袭性纤维瘤病的CT表现,以期提高对本病的认识及诊断水平。方法:收集经病理证实的9例腹外型侵袭性纤维瘤病患者的资料,回顾性分析其CT表现。结果:9例腹外型侵袭性纤维瘤病中,位于软组织7例(包括胸壁4例、颈部2例、大腿1例),位于骨骼2例(骶骨及颌骨各1例)。7例软组织肿瘤CT平扫表现为密度均匀的中等密度4例、略低密度3例,均与肌肉组织分界不清,骨质侵蚀破坏3例;增强扫描轻中度强化3例、明显强化4例。2例骨肿瘤CT平扫表现为膨胀性骨质破坏,周缘硬化边1例,肿瘤内肿瘤性骨小梁1例,1例增强扫描呈轻度强化。结论:腹外型侵袭性纤维瘤病是一种少见的中间性软组织肿瘤,CT表现具有一定的特征性,确诊仍依赖于病理学检查。

Objective： To analyze the CT characters of extra-abdominal aggressive fibromatosis,in order to achieve more information about the disease and to improve the diagnostic accuracy.Methods： The CT appearances of extra-abdominal aggressive fibromatosis in nine cases were reviewed.All the cases were confirmed by operation and pathology.Results： In the nine cases of extra-abdominal aggressive fibromatosis,seven tumors were located in soft tissue（including five in chest wall,two in neck and one in thigh） and two in bone（sacrum and maxillary respectively）.On pre-contrast CT images,seven tumors in soft tissue showed equal or mild lower density than muscle,with bone destruction in three cases.On enhanced CT images,three cases showed mild to moderate enhancement,and four showed significantly enhancement.Aggressive fibromatosis of bone were expansive lytic with bony rim in one case and trabecular bone in the other case.Conclusion： Aggressive fibromatosis is a rare soft tissue tumor.It has certain characteristic performance of CT,yet final diagnosis should be based on histopathology.