摘要
患儿男,5岁。面部、躯干、四肢出现色素减退斑5年。皮肤科情况:面部、躯干、四肢可见特殊形状的色素减退斑,大多数白斑呈线状或旋涡状,边界清楚。激光共聚焦扫描显微镜检查(手臂):与周围皮肤对照,浅色斑区基底层色素减少,基底细胞环大致存在,部分基底环可见点状缺失,真皮乳头及浅层可见少许嗜黑素细胞及稀疏炎细胞浸润。诊断:脱色性色素失禁症。
A 5-year-old boy presented with macular hypopigmentation of special patterns over the face,trunk and limbs 5 years before.Physical examination showed bizarre and patterned whitish patches spread over the face,trunk and limbs,and the most of whitish patches manifested as line or vortex with distinct boundary.Laser confocal scanning microscope showed that compare with the normal skin,pigment in the stratum basale of the whitish patches was decreased,the rings of the cells in the stratum basale were roughly existed with pointlike lack in some part,very few melanocytes and inflammatory infiltrates were seen in the dermal papilla and the shallow layer.Diagnosis of incontinentia pigmenti achromicans was made.
出处
《中国皮肤性病学杂志》
CAS
北大核心
2012年第6期530-531,共2页
The Chinese Journal of Dermatovenereology
关键词
色素失禁症
无色素性
Incontinentia, pigmenti aehromians