小儿结节性硬化症的平扫CT影像和临床价值

CT features and clinical value of tuberous sclerosis in children with plain CT scanning

目的总结CT平扫在小儿结节性硬化症中的影像表现和临床诊断价值。方法回顾性分析我院41例结节性硬化症患儿的颅脑CT表现,并经临床共同确诊。结果 41例小儿结节性硬化症CT平扫表现为颅内钙化和/(或)非钙化结节。结节发生于室管膜下40例(97.5%),在首次扫描或复诊扫描中,结节钙化发现率100%;结节发生于皮质或皮质下11例(26.8%);脑实质内可见孤立的斑片状钙化10例(24.3%);双侧侧脑室扩大20例(48.8%)。结论小儿结节性硬化症的颅内结节多为室管膜下钙化或高密度结节。CT平扫对颅内高密度或钙化结节具有高度特异性,是诊断小儿结节性硬化症的首选方法。

Objective To study the CT features and diagnostic value of tuberous sclerosis in children with Plain CT scanning. Methods 41 children with tuberous sclerosis diagnosed by clinical data and CT were reviewed. Results 41 cases displayed intracranial calcification and/or non-calcified tubercles, Situating in su- bendyma （40 cases, accounting for 97.5 % ）, any calcified tubercle can be showed （ 100% ） ai first or again CT scanning, cortex or subcortex 11 cases（26. 8% ）. There was solitary calcification patches in parenchyma（ 10 ca- ses,24. 3 % ）, and 20 cases showed enlarged bliateral ventricles （48. 8% ）. Conclusion Intracranial tubercles of tuberous sclerosis in children often were calcified tubercles in subendyma. Plain CT Scanning is highly specif- ic for high-density or calcified tubercles, serving as a top choice in diagnosis of tuberous sclerosis.