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长QT综合征的基因检测及诊疗进展 被引量:7

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摘要 LQTS指具有心电图上QT间期延长,T波异常,易产生室性心律失常,尤其是尖端扭转型室速(TdP),晕厥和猝死的一组综合征。LQTS是最先发现的也是最常见的离子通道病,分为遗传性和获得性两种。遗传性LQTS按照是否伴有耳聋又可区为两种形式:RWS综合征和JLNS综合征。
出处 《江西医药》 CAS 2012年第5期416-419,共4页 Jiangxi Medical Journal
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