结节性硬化的CT诊断

The CT dignosis of tuberous sclerosis

目的探讨结节性硬化症的CT诊断价值。方法回顾性分析我院10年来经病理证实的6例结节性硬化的临床表现和CT特征,并结合有关文献进行分析。结果 6例患者均以智力低下、癫痫就诊,2例出现肾血管平滑肌脂肪瘤(AML),2例见巨细胞星形细胞瘤。结论结节性硬化具有特征性的临床表现,CT能清晰显示病变的部位、大小、形态、密度及波及范围,CT是结节性硬化诊断的一种重要的检查方法。

Objective To study the CT features of tuberous sclerosis. Methods The CT and clinical features of six cases of tuberous sclerosis confirmed by pathology were retrospectively analysed. Results All patients suffered from epilepsy and hypophrenia, two patients had multiple angimyolipoma（AML）, two patients had giant cell astrocytoma. Conclusion There are characteristic clinical features and CT appearances in tuberous sclerosis. CT can clearly demonstrate the location, size, shape, density and extent of the lesions, which is of great value for the diagnosis of tuberous sclerosis.