摘要
Dravet综合征(DS)亦称婴儿严重肌阵孪性癫痫,是儿童期起病的由遗传因素引起的罕见的癫痫性脑病,病程延伸到成年,其总体发病率为1/40000~1/20000,男:女比例约为2:1。现对DS综述如下。1临床特点。发热、感染或疫苗接种、光以及图形刺激均是DS发病的重要诱发因素。有时光环境中的自我刺激在闭眼亦可诱发,然而光刺激到20岁时就不会再诱发DS发作;其他的诱因包括热水浴、体育锻炼、情感反应、喧闹环境等。
出处
《临床神经病学杂志》
CAS
北大核心
2012年第4期316-317,共2页
Journal of Clinical Neurology
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