小脑扁桃体延髓联合畸形型164例MR诊断

MR diagnosis of Arnold-Chiari malformation type I(analysis of 164 cases)

评价 Arnold- Chiari畸形 ( ACM)的 MR诊断价值。方法 :对我院 1990年 1月至 1999年 12月间 164例临床未明确诊断的 ACM 型患者进行 MR检查 ,总结并分析其影像表现。结果 :164例中 ,60 %脊髓萎缩 ( 99/164) ;80 %出现不同程度脊髓空洞 ( 12 3/164) ;71%延、颈髓交界处屈曲成角 ( 117/164) ;75%合并其他畸形 ( 12 3/164) ;70 %合并颅颈交界处骨结构畸形 ( 115/164)。结论 :MR是诊断 ACM的首选方法 ,并能准确查明其合并畸形、脊髓空洞范围及程度。

Objective:To evaluate the diagnostic value of MR for ACM.Methods:164 patients,with obscure clinical diagnosis from Jan.1990 to Dec.1999,were examed by a 1.0T superconductive MR system.The diagnosis of ACM Type Ⅰ was established in all cases and their MR appearances were summarized and analysed. Results:In all cases,60%(99/164)patients had a variable degree of syringohydromyelia;71%(117/164)had cervicomedullary kinking;75%(123/164)were associated with other malformation;70%(115/164)were associated with craniocervical junction malformation.Conclusion:MR has been proved to be the best method in diagnosis of ACM,and it can be used to find out accurately the associated malformation,degree and range of syringohydromyelia.