血友病性假瘤的MDCT表现

Imaging Features of Hemophilic Pseudotumor on Multidetector Computed Tomography

目的提高对血友病性假瘤多层螺旋CT(MDCT)表现特点的认识。方法回顾性分析16例经临床证实的血友病性假瘤患者的CT影像学特点。16例均行MDCT检查,并行冠状位及矢状位重组,着重分析假肿瘤的部位、大小、形态、密度、强化方式及骨质改变。结果 16例经实验室检查确诊为血友病A型12例,血友病B型4例。16例中12例有外伤史。主要影像学改变为溶骨性破坏14例,软组织肿胀、肿块13例。结论血友病性假瘤影像学特征取决于病变的首发部位和出血程度。CT对血友病性假瘤的诊断具有一定的临床实用价值,对临床治疗具有重要的指导意义。

Objective To analyze the imaging characteristics of hemophilic pseudotumor retrospectively on multidetector computed tomography for improving the level of diagnosis.Methods CT imaging features of 16 cases of hemophilic pseudotumor were analyzed retrospectively.All cases underwent preoperative MDCT studies and axial CT images and coronally and sagittally reformed images were obtained on the advanced workstation.Notes were made on tumor location,diameter,shape,margin,pattern of calcification,density,enhancement pattern and bone destruction.Results All 16 patients were diagnosed with hemophilic pseudotumor by their laboratory examinations（12 hemophilic A cases and 4 hemophilic B cases）.Twelve patients sustained an injury prior to the development of pseudotumor.Main image findings included osteolysis lesion（14 cases）,soft tissue swelling or lump（13 cases）.Conclusion The radiologic characteristics of hemophilic pseudotumor depend on the initial site and extent of hemorrhage.CT scanning plays important roles in the diagnosis of hemophilic pseudotumor.