伴恶性纤维组织细胞瘤去分化股骨远端脂肪肉瘤一例

Dedifferentiated liposarcoma in the distal femur accompanied by malignant fibrous histiocytoma:a case report

原发性骨内脂肉瘤（Primary intraosseous liposa-rcoma）是一种罕见的、恶性度很高的骨骼系统肿瘤，原发于骨髓内的脂肪组织。自Stewort于1931报道第1例以来，目前国内外仅报道有几十例，并且都是以个案的形式出现。据WHO统计，骨内脂肪肉瘤占原发骨肿瘤的0.04％，占恶性骨肿瘤的0.08％。我科收治1例经术后病理检查确诊的右股骨远端脂肪肉瘤，现报道如下。

Primary intraosseous liposarcoma was a rare and mahgnant tumor ot the skeletal system, it originated from the intraosseous adipose tissue. Since the first case was reported in 1931, there were only dozens of cases reported at home and abroad now, without the unified standard for diagnosis and treatment. Recently, a patient with intraosseous dedifferentiated liposarcoma was adopted by our department. Neither recurrence nor metastasis had been detected for 2 months after surgery.