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Panayiotopoulos综合征临床及脑电图特征

Clinical and electroencephalographic characteristics of epilepsy with Panayiotopoulos Syndrome
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摘要 目的 Panayiotopoulos综合征(Panayiotopoulos Syndrome,PS)是一种以自主神经系统症状为主要临床表现的儿童癫痫综合征。本文旨在总结PS的临床及脑电特征。方法收集13例PS患儿的临床、脑电图资料进行分析,部分进行了治疗及随访研究。结果 13例PS患儿,男6例,女7例;起病年龄3岁2个月~10岁8个月。临床以自主神经症状为主,如呕吐、恶心、头痛、面色苍白、腹痛、瞳孔扩大等症状。发作时8例明显意识障碍,4例轻度意识障碍,1例无明显意识障碍。10例发作表现为自主神经持续状态,其中1例发作时间达5h。其余发作形式包括眼球偏斜,部分有眼球偏斜伴头部偏斜。4例出现一侧面部及一侧上下肢抽搐,1例出现全面强直阵挛发作。脑电图特征为所有13例患儿脑电图*清醒期有痫样放电7例,睡眠期均有痫样放电。痫样放电以后头部为主7例,前头部、中央中颞区也可见痫样放电。5例患儿仅出现一次发作。7例口服抗癫痫药物均得到良好控制。发作前后精神发育均正常。结论 PS为儿童良性癫痫,临床发作以自主神经症状为主,持续时间较长,脑电监测以后头部放电为主,预后良好。 Objective: Panayiotopoulos Syndrome is a type of childhood epilepsy characterized by a specific clinical symptom of autonomic nervous system.This study aimed to investigate the clinical and electroencephalographic characteristics of epilepsy with Panayiotopoulos Syndrome.Method: The data of the Clinical and electroencephalographic characteristics were collected and analyzed in 13 patients with PS,some were carried out the study of treatment and follow-up.Result: Of the 13 patients,6 were male,and 7 were female.The age of onset was from 3 years and 2 months to 10 wears 8 months.The clinical symptom of autonomic nervous system was predominant seizure type in all PS,such as vomiting,nausea,headache,pale complexion,abdominal pain and dilated pupil.8 patients presented serious consciousness disorders,4 patients presented mild consciousness disorders and one patient was normal.10 patients with PS presented autonomic status epilepticus,and seizure time lasted for 5 hours in one patient.The other form of seizure included eyeball deviation or accompanied head deviation.4 paients presented convulsion in unilateral face or unilateral upper and lower extremity.one patient presented generalized tonic clonic seizures.13 patients had normal rhythm in electroencephalography.7 patients had epileptic discharge in awake period,and all patients had epileptic discharge in sleep period.Epileptic discharge in occiput had been observed in 7 patients,and discharge of other location in some patients had been seen too.5 patients had only one seizure.7 patients who were administered antiepileptic medicine had completely free of seizure.Intelligence and movement development were normal before and after seizure.Conclusion: PS was a benign epilepsy characterized by long time of autonomic status.Epileptic discharge was predominant over occiput.PS had favourable prognosis.
作者 叶小飞 杨斌
出处 《中国优生与遗传杂志》 2013年第2期119-120,122,共3页 Chinese Journal of Birth Health & Heredity
关键词 Panayiotopoulos综合征 临床 脑电图 Panayiotopoulos Syndrome Electroencephalography Clinical character
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