多系统淋巴管肌瘤病的CT表现

CT Appearances of Multi-system Lymphangiomymoatosis

目的:分析多系统淋巴管肌瘤病(LAM)的CT表现,提高对其疾病的进一步认识。材料与方法:回顾性分析10例经病理或随访证实的多系统LAM患者的CT表现。结果:10例LAM均出现肺部异常,CT表现为:两肺多发或广泛分布薄壁小囊状影10例;纵隔淋巴结肿大和乳糜胸水各2例,气胸1例,肺磨玻璃样改变1例。6例出现腹部异常,CT表现为:肾血管平滑肌脂肪瘤(AML)4例,其中1例合并肝AML;腹膜后多发淋巴管肌瘤(LALM)和乳糜腹水各1例。结论:淋巴管肌瘤病的CT表现有一定特征性,同时行胸腹部CT检查有助于本病的全面认识和早期诊断。

Purpose ： To analyze the CT appearances of multi-system lymphangioleiomyomatosis （LAM） , and make a further understanding of the diseases. Materials and Methods： 10 Cases＇ CT findings with LAM confirmed by pathology or following up were reviewd retrospectively. Results： All cases were abnormal in the lung , CT imagings showed pulmonary muhiple and small thin - wall cystic shadows （ n = 10） ; mediastinal lymph node intumesced （ n = 2 ） , chylothorax （ n = 2 ） , pneumothorax （n = 1 ）, lung ground glass （ n = 1 ）. 6 cases were abnormal in the abdomen, CT imagings showed kidney hamar- tom （ n = 4）, liver hamartom （ n = 1 ）, LALM and chylous ascites （ n = 1 ）. Conclusion ： LAM＇s CT image is characteristic , it is helpful to overall recognization and early diagnosis that chest and abdomen CT scan together.