先天性胆管囊性扩张合并胰胆管合流异常

Congenital cystic cholangiectasis with abnormal pancreaticocholangial connection

目的 探讨先天性胆管囊性扩张症的诊断与治疗。方法 经内镜逆行胰胆管造影 (ER CP)对该症作出诊断。结果 从本院ERCP 12 5 4例中检出 15例 ,本组有 8例合并胰胆管合流异常 ,占5 3 3% ;同时有 8例合并其他胰胆疾病 ,占 5 3 3%。结论 诊断以ERCP为首选 ,能确诊并可明确有无合并胰胆管合流异常。该症治疗采用早期囊肿切除同时行胆管空肠吻合术 。

Objective The relationship between congenital cystic cholangiectasis and abnormal pancreaticocholangial connection was explored Methods Endoscopic retrograde cholangiopancreatography (ERCP) was applied Results 15 patients were diagnosed to have congenital cystic cholangiectasis by ERCP from 1254 cases, of which 8 (53 30%) being associated with abnormal pancreaticocholangial connection Conclusion The rare disorder of congenital cystic cholangiectasis with or without abnormal pancreaticocholangial connection can clearly be visualized and diagnosed by ERCP Early excision of the cystic dilatation with intestinal diversion offers favorable results