摘要
Extrahepatic or prehepatic portal vein cavernoma and thrombosis is a more common condition in children than that in adult patients with extrahepatic or prehepatic portal vein obstruction （EHPVO）, which involves approximately 30% of children with portal hypertension and can involve all the portal hypertension complications. Cavernomatous transformation of the portal vein is common after portal thrombosis in non-cirrhotic patients. This challenging situation is relatively more frequent after liver transplantation, particularly in pediatric recipients. Acute bleeding from esophageal and gastric varices is temporarily treated by sclerotherapy or variceal banding. Children who experience continued bleeding despite medical management or who experience clinically significant hypersplenism are referred for surgery.
Extrahepatic or prehepatic portal vein cavernoma and thrombosis is a more common condition in children than that in adult patients with extrahepatic or prehepatic portal vein obstruction （EHPVO）, which involves approximately 30% of children with portal hypertension and can involve all the portal hypertension complications. Cavernomatous transformation of the portal vein is common after portal thrombosis in non-cirrhotic patients. This challenging situation is relatively more frequent after liver transplantation, particularly in pediatric recipients. Acute bleeding from esophageal and gastric varices is temporarily treated by sclerotherapy or variceal banding. Children who experience continued bleeding despite medical management or who experience clinically significant hypersplenism are referred for surgery.
