鼻腔恶性外周神经鞘肿瘤1例

A case of nasal malignant peripheral nerve sheath tumor

患者，女，52岁，因左侧鼻塞1年余入院。鼻塞呈持续性，进行性加重，伴咽干，无流涕、鼻出血、嗅觉障碍、头痛、复视。鼻内镜下见左侧鼻腔内一肿物填塞后鼻孔及鼻咽部，色灰白，质稍硬，表面光滑可见毛细血管扩张，无破溃（图1），鼻中隔稍右偏。CT示：左侧鼻腔内见类圆形软组织密度影（图2），CT值约37HU，最大截面积约2．3cm×1．3cm，边界清晰，与上鼻道相连续，左侧上颌窦、筛窦黏膜增厚；鼻腔及窦壁骨质均未见破坏。

Summary The 52-year-old female patient complained of persistent and progressive obstruction in left nasal cavity for more than 1 years. A grey, hard and smooth tumor with telangiectasia, were seen plugged in left post- nostrils and nasopharynx. CT scanning showed a tumor in the left nasal cavity. Post-operational pathologic diagno sis was peripheral nerve sheath tumors of nasal cavity.