儿童血友病的急救处理

Emergency management of childhood hemophilia

普通门诊和急救科医务人员通常缺乏血友病诊治经验，因此，建立针对血友病的急救体系和诊疗标准十分必要。急救科医务人员需要识别未获诊断的出血性疾病患儿，对急诊就诊的血友病患儿应进行出血状况评估，尽快给予凝血因子替代治疗等止血措施，并要警惕抑制物的生成。

Doctors and nurses from general outpatient and emergency department usually lack the treatment experience of hemophilia, therefore, emergency system and diagnostic criteria for hemophilia is essential. Physicians of emergency department should be trained on identifying the undiagosed patients with inherited bleeding disorders and assessing the condition of bleeding. Prompt clotting factors replacement therapy should be given to the patients with hemophilia once bleeding is suspected. Physicians should be aware that inhibitors make the emerzency treatment more comohcated.