血友病特定出血部位的治疗

Bleeding management of special sites for hemophilia patients

血友病作为先天遗传性出血性疾病，出血为其主要表现。最常见的出血部位为关节、肌肉。颅内出血、消化道出血将危及生命，而特殊部位（如眼部、咽喉部等）出血也十分重要。对血友病患儿出血的正确识别和恰当治疗至关重要，将减少致死致残，提高患儿生活质量。本文介绍血友病患儿的几个特定部位的出血治疗。

As one of congenital bleeding diseases, the bleeding is the most important manifestation in hemophilia patients. The most common bleeding sites are joints and muscles ,the most life-threatening bleed- ings are intracranial hemorrhage and gastrointestinal hemorrhage, and some special sites （like eye, throat） are also very important. The correct identification and appropriate management for the bleeding episode are the most important issues for the reduction of modality and morbidity and the improvement of their life quality improvement. In this review, we will discuss the management of several special sites in hemophilia patients.